論文

2014年12月

[Perirenal malignant perivascular epithelioid cell tumor originating from right retroperitoneum: a case report].

Hinyokika kiyo. Acta urologica Japonica
  • Shotaro Nakanishi
  • ,
  • Minoru Miyazato
  • ,
  • Kan Yonemori
  • ,
  • Tomoko Tamashiro
  • ,
  • Naoki Yoshimi
  • ,
  • Seiichi Saito

60
12
開始ページ
627
終了ページ
30
記述言語
日本語
掲載種別
研究論文(学術雑誌)

A 51-year-old woman was admitted to our hospital for detailed examinations and medical treatment against the right retroperitoneum tumor and liver lesions. Computed tomography showed a 20 cm diameter enhanced mass in the right perirenal space and multiple liver metastases. Pathological examination by needle biopsy revealed a perivascular epithelioid cell tumor (PEComa). With weekly administration of a mTOR inhibitor, Temsirolimus, the tumor was reduced by about 20% one month later. The maximal response was stable disease due to RECIST v 1. 1. However, shortly after the minimal response, the disease showed progression. She died about five months after the start of molecular targeted therapy. In regard to the origin of PEComa, our report is the fifth in Japan as a case of retroperitoneal origin to the best of our knowledge.

リンク情報
PubMed
https://www.ncbi.nlm.nih.gov/pubmed/25602479
ID情報
  • ISSN : 0018-1994
  • PubMed ID : 25602479

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