2016年11月
Reversible striatal hypermetabolism in chorea associated with moyamoya disease: a report of two cases
CHILDS NERVOUS SYSTEM
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- 巻
- 32
- 号
- 11
- 開始ページ
- 2243
- 終了ページ
- 2247
- 記述言語
- 英語
- 掲載種別
- 研究論文(学術雑誌)
- DOI
- 10.1007/s00381-016-3111-5
- 出版者・発行元
- SPRINGER
Background The pathophysiological mechanism of chorea as a presentation of pediatric moyamoya disease remains unknown, although ischemia is suspected as a likely cause. The authors describe two cases of pediatric moyamoya disease, both of which presented with hemichorea in the stable phase after successful bypass surgery. Clinical Presentation
Cerebral blood flow was almost normal in one case and decreased in the basal ganglia and watershed area in the other case due to infarcts occurring before surgery. In both cases, F-18-fluorodeoxyglucose positron emission tomography revealed elevated glucose metabolism in the corresponding side of the striatum, which reverted to normal after recovery from chorea. Magnetic resonance angiography revealed a dilated and extended lenticulostriate artery at the exact site of the hypermetabolic lesion.
Cerebral blood flow was almost normal in one case and decreased in the basal ganglia and watershed area in the other case due to infarcts occurring before surgery. In both cases, F-18-fluorodeoxyglucose positron emission tomography revealed elevated glucose metabolism in the corresponding side of the striatum, which reverted to normal after recovery from chorea. Magnetic resonance angiography revealed a dilated and extended lenticulostriate artery at the exact site of the hypermetabolic lesion.
- リンク情報
- ID情報
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- DOI : 10.1007/s00381-016-3111-5
- ISSN : 0256-7040
- eISSN : 1433-0350
- PubMed ID : 27193011
- Web of Science ID : WOS:000387230600032