論文

国際誌
2019年1月23日

Left colic artery aneurysm rupture after stent placement for abdominal aortic aneurysm associated with neurofibromatosis type 1.

Surgical case reports
  • Kazuki Moro
  • ,
  • Hitoshi Kameyama
  • ,
  • Kaoru Abe
  • ,
  • Junko Tsuchida
  • ,
  • Yosuke Tajima
  • ,
  • Hiroshi Ichikawa
  • ,
  • Masato Nakano
  • ,
  • Mayuko Ikarashi
  • ,
  • Masayuki Nagahashi
  • ,
  • Yoshifumi Shimada
  • ,
  • Kaori Kato
  • ,
  • Takeshi Okamoto
  • ,
  • Hajime Umezu
  • ,
  • Emmanuel Gabriel
  • ,
  • Masanori Tsuchida
  • ,
  • Toshifumi Wakai

5
1
開始ページ
12
終了ページ
12
記述言語
英語
掲載種別
研究論文(学術雑誌)
DOI
10.1186/s40792-019-0570-4

BACKGROUND: Neurofibromatosis type 1 (NF1) is an autosomal dominant disease of the skin and soft tissue. Aneurysms associated with NF1 can occur, but a secondary aneurysm rupture is very rare, with very few cases reported in literature. CASE PRESENTATION: We describe the case of a 67-year-old female with NF1 who underwent endovascular aneurysm repair (EVAR) for an abdominal aortic aneurysm (AAA) rupture. She developed a type Ib endoleak requiring a redo-EVAR. Eighteen days after her primary operation, she was found to have two new left colic artery aneurysms. She required emergency surgery consisting of a left hemicolectomy and transverse colon colostomy. Pathology showed neurofibromatous changes to the peri-vasculature tissue, consistent with her underlying disease. CONCLUSIONS: Although rare, secondary aneurysms can occur following AAA repair. Patients with soft tissue connective tissue disorders, like NF1, may be at an increased risk for development of these secondary aneurysms. Endovascular repair appears to be a safe approach for NF1 patients with AAA, but endovascular management can be challenging in the setting of NF1. Surgeons should be ready to convert to open surgery if the patient displays persistent signs of bleeding or structural changes related to connective tissue disorders like NF1.

リンク情報
DOI
https://doi.org/10.1186/s40792-019-0570-4
PubMed
https://www.ncbi.nlm.nih.gov/pubmed/30673931
PubMed Central
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6346692
ID情報
  • DOI : 10.1186/s40792-019-0570-4
  • PubMed ID : 30673931
  • PubMed Central 記事ID : PMC6346692

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