The authors conducted a nationwide survey of women with moyamoya disease on their pregnancy and delivery experiences. In pregnant women who were known to have moyamoya disease, the incidence of perinatal cerebrovascular attacks was low. Although caesarian section was mainly adopted in these cases, there was no evidence that vaginal delivery should be avoided. On the other hand, serious cerebral hemorrhage or infarction was reported in those patients who had not been diagnosed with moyamoya disease before their pregnancy. To make pregnancy and delivery of the female patients safer, cooperation between obstetrician and neurosurgeons is important, and guidelines on pregnancy management for female patients with moyamoya disease should be established.