Aug, 2019
A Patient with Type 3 Autoimmune Polyglandular Syndrome who Developed Systemic Lupus Erythematosus 8 years after the Diagnosis of Autoimmune Hepatitis.
Acta medica Okayama
- Volume
- 73
- Number
- 4
- First page
- 367
- Last page
- 372
- Language
- English
- Publishing type
- Research paper (scientific journal)
- DOI
- 10.18926/AMO/56940
Eight years prior to her present admission, a 61-year-old Japanese woman was diagnosed with autoimmune hepatitis, slowly progressive insulin-dependent diabetes mellitus, and chronic thyroiditis; she had been treated with oral prednisolone (PSL). After she suddenly discontinued PSL, she newly developed systemic lupus erythematosus. A combination therapy of oral PSL and intravenous cyclophosphamide resulted in remission. She was finally diagnosed with autoimmune polyglandular syndrome (APS) type 3 (3A ,3B, 3D), complicated with four different autoimmune diseases. Since patients with type 3 APS may present many manifestations over a long period of time, they should be carefully monitored.
- Link information
- ID information
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- DOI : 10.18926/AMO/56940
- Pubmed ID : 31439961