© 2020 The Authors Early diagnosis of primary central nervous system lymphoma (PCNSL) in the extra-axial region is difficult due to the corresponding atypical clinical symptoms and radiological findings. This case report documents the rare diagnosis and treatment of PCNSL of the bilateral Bochdalek's flower baskets (protrusions of the fourth ventricle choroid plexus into the cerebellopontine angles). The patient initially presented with subacute vertigo and left hearing loss. Radiological findings included symmetrical mass lesions in the bilateral cerebellopontine angles. An open biopsy enabled the pathological diagnosis of diffuse large B-cell lymphoma. The primary tumors were successfully removed through chemoradiation. However, the patient died six months after treatment completion due to cerebrospinal dissemination. PCNSL should be considered when diagnosing brain tumors with atypical symptoms and radiological findings.